Relapsing polychondritis is a rare autoimmune disease that attacks cartilage throughout the body — including the cartilages of the larynx and trachea. As the laryngeal framework degrades, the voice softens and the airway narrows. In severe cases the trachea collapses on inspiration, causing life-threatening stridor.
Management
Management requires systemic immunosuppression — typically corticosteroids and steroid-sparing agents — along with close monitoring of the airway. When tracheal involvement is severe, tracheotomy or airway stenting may be necessary.
This page will be expanded with endoscopic photographs and additional clinical detail.